There has been much confusion about the understanding of congenital venous malformations for a long time, for which the misdiagnosis and wrong treatment often occur in clinical practice so that standardizing the medical processes is an urgent matter. In Chapter 6 of Management of Chronic Venous Disease Clinical Practice Guidelines of the European Society for Vascular Surgery (ESVS) published in the ESVS official journal European Journal of Vascular and Endovascular Surgery in June 2015, the classification of congenital vascular malformations was discussed, paying particular attention to the etiology, clinical characteristics, diagnosis and management of congenital venous malformations, as well as the complex congenital venous malformations affecting the venous system, such as Klippel-Trenaunay and Parkes-Weber syndrome. This will be of great significance for the further improvement of their diagnosis and treatment.